Transposition of the great arteries (TGA) with intact ventricular septum (IVS) has very favorable short- and long-term surgical outcome. Although rare, when associated with persistent pulmonary hypertension (PPH), it exhibits significant mortality risk and management challenges. We report the case of a neonate with TGA with IVS and PPH who underwent successful early surgical repair with emphasis on clinical management and review of the literature.
Keywords: congenital heart disease; neonate; persistent pulmonary hypertension; transposition of the great arteries with intact ventricular septum.
© The Author(s) 2014.