Persistent Pulmonary Hypertension in a Neonate With Transposition of Great Arteries and Intact Ventricular Septum: A Case Report and Review of the Literature

World J Pediatr Congenit Heart Surg. 2015 Jul;6(3):462-5. doi: 10.1177/2150135114558848.

Abstract

Transposition of the great arteries (TGA) with intact ventricular septum (IVS) has very favorable short- and long-term surgical outcome. Although rare, when associated with persistent pulmonary hypertension (PPH), it exhibits significant mortality risk and management challenges. We report the case of a neonate with TGA with IVS and PPH who underwent successful early surgical repair with emphasis on clinical management and review of the literature.

Keywords: congenital heart disease; neonate; persistent pulmonary hypertension; transposition of the great arteries with intact ventricular septum.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Cardiomyopathy, Hypertrophic / complications*
  • Cardiomyopathy, Hypertrophic / congenital
  • Female
  • Humans
  • Hypertension, Pulmonary / diagnosis
  • Hypertension, Pulmonary / etiology*
  • Infant, Newborn
  • Transposition of Great Vessels / complications*
  • Ventricular Septum*