Abstract
Primary myositis (or inflammatory myopathies) comprises three main groups of diseases, based on clinical and immunohistochemical characteristics: polymyositis (PM), dermatomyositis (DM) and inclusion body myositis. Their clinical presentation and course are disparate, but a common characteristic is immune dysfunction-related inflammation of the striated muscles. Their etiologies are still not fully elucidated but associate environmental and, to a lesser degree, genetic factors. Nevertheless, considerable progress has recently been made in the understanding and management of these diseases.
MeSH terms
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Anti-Inflammatory Agents / therapeutic use
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Biopsy
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Dermatomyositis / classification
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Dermatomyositis / diagnosis*
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Dermatomyositis / epidemiology
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Dermatomyositis / etiology
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Dermatomyositis / therapy*
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Humans
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Immunohistochemistry
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Myositis, Inclusion Body / classification
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Myositis, Inclusion Body / diagnosis*
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Myositis, Inclusion Body / epidemiology
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Myositis, Inclusion Body / etiology
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Myositis, Inclusion Body / therapy*
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Plasmapheresis
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Polymyositis / classification
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Polymyositis / diagnosis*
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Polymyositis / epidemiology
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Polymyositis / etiology
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Polymyositis / therapy*
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Prognosis
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Steroids
Substances
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Anti-Inflammatory Agents
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Steroids