Abstract
A case of a 38-year old man with a common variable immunodeficiency syndrome (CVID) is demonstrated who suffered at the same time from a histologically proven inclusion body myositis (IBM). The myositis did not resolve after institution of regular intravenous IgG infusions. This case demonstrates a very long lasting benign course of IBM. The occurrence with CVID may be a clinical hint for a viral pathogenesis of IBM. So far only two similar cases are reported in the literature.
MeSH terms
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Adult
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Arthralgia / complications
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Arthralgia / physiopathology
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Azathioprine / therapeutic use
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Common Variable Immunodeficiency / complications*
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Common Variable Immunodeficiency / drug therapy
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Common Variable Immunodeficiency / physiopathology
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Fatigue / complications
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Fatigue / physiopathology
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Humans
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Immunoglobulins, Intravenous / therapeutic use
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Male
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Myositis, Inclusion Body / complications*
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Myositis, Inclusion Body / drug therapy
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Myositis, Inclusion Body / physiopathology
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Prednisolone / therapeutic use
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Tenosynovitis / complications
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Tenosynovitis / physiopathology
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gamma-Globulins / therapeutic use
Substances
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Immunoglobulins, Intravenous
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gamma-Globulins
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Prednisolone
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Azathioprine