Common variable immunodeficiency (CVID) and inclusion body myositis (IBM)

Immunobiology. 2000 Aug;202(2):199-203. doi: 10.1016/S0171-2985(00)80067-4.

Abstract

A case of a 38-year old man with a common variable immunodeficiency syndrome (CVID) is demonstrated who suffered at the same time from a histologically proven inclusion body myositis (IBM). The myositis did not resolve after institution of regular intravenous IgG infusions. This case demonstrates a very long lasting benign course of IBM. The occurrence with CVID may be a clinical hint for a viral pathogenesis of IBM. So far only two similar cases are reported in the literature.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Arthralgia / complications
  • Arthralgia / physiopathology
  • Azathioprine / therapeutic use
  • Common Variable Immunodeficiency / complications*
  • Common Variable Immunodeficiency / drug therapy
  • Common Variable Immunodeficiency / physiopathology
  • Fatigue / complications
  • Fatigue / physiopathology
  • Humans
  • Immunoglobulins, Intravenous / therapeutic use
  • Male
  • Myositis, Inclusion Body / complications*
  • Myositis, Inclusion Body / drug therapy
  • Myositis, Inclusion Body / physiopathology
  • Prednisolone / therapeutic use
  • Tenosynovitis / complications
  • Tenosynovitis / physiopathology
  • gamma-Globulins / therapeutic use

Substances

  • Immunoglobulins, Intravenous
  • gamma-Globulins
  • Prednisolone
  • Azathioprine