ER-associated ubiquitin ligase HRD1 programs liver metabolism by targeting multiple metabolic enzymes

Nat Commun. 2018 Sep 10;9(1):3659. doi: 10.1038/s41467-018-06091-7.

Abstract

The HMG-CoA reductase degradation protein 1 (HRD1) has been identified as a key enzyme for endoplasmic reticulum-associated degradation of misfolded proteins, but its organ-specific physiological functions remain largely undefined. Here we show that mice with HRD1 deletion specifically in the liver display increased energy expenditure and are resistant to HFD-induced obesity and liver steatosis and insulin resistance. Proteomic analysis identifies a HRD1 interactome, a large portion of which includes metabolic regulators. Loss of HRD1 results in elevated ENTPD5, CPT2, RMND1, and HSD17B4 protein levels and a consequent hyperactivation of both AMPK and AKT pathways. Genome-wide mRNA sequencing revealed that HRD1-deficiency reprograms liver metabolic gene expression profiles, including suppressing genes involved in glycogenesis and lipogenesis and upregulating genes involved in glycolysis and fatty acid oxidation. We propose HRD1 as a liver metabolic regulator and a potential drug target for obesity, fatty liver disease, and insulin resistance associated with the metabolic syndrome.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adenylate Kinase / metabolism
  • Animals
  • Body Weight
  • Diet, High-Fat
  • Endoplasmic Reticulum / metabolism*
  • Endoplasmic Reticulum-Associated Degradation*
  • Enzyme Activation
  • Fatty Acids / metabolism
  • Gene Deletion
  • Gene Expression Regulation
  • Genome-Wide Association Study
  • Glycolysis
  • HEK293 Cells
  • Hep G2 Cells
  • Humans
  • Lipogenesis
  • Liver / metabolism*
  • Mice
  • Mice, Inbred C57BL
  • Obesity / metabolism
  • Proteome
  • Proteomics
  • Triglycerides / metabolism
  • Ubiquitin-Protein Ligases / metabolism*
  • Ubiquitination

Substances

  • Fatty Acids
  • Proteome
  • Triglycerides
  • Syvn1 protein, mouse
  • Ubiquitin-Protein Ligases
  • Adenylate Kinase