Abstract
IgG4-related disease (IgG4-RD) is a recently described entity characterized by lymphoplasmacytic infiltrates, usually mimicking tumors, affecting almost every organ or system. Nevertheless, serosal involvement has been rarely reported. In this article, we report two cases of IgG4-RD with serosal involvement and review the literature. Because of the varied clinical pictures found in our review, we suggest a new terminology for the description of IgG4-RD with serosal involvement.
Keywords:
IgG4-related disease; Pericardium; Peritoneum; Pleura.
MeSH terms
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Adult
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Aged
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Aged, 80 and over
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Autoimmune Diseases / diagnosis
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Autoimmune Diseases / drug therapy
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Autoimmune Diseases / immunology*
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Biomarkers / blood
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Drug Therapy, Combination
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Female
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Humans
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Immunoglobulin G / blood*
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Immunosuppressive Agents / therapeutic use
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Male
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Middle Aged
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Pericardial Effusion / diagnosis
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Pericardial Effusion / drug therapy
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Pericardial Effusion / immunology*
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Pericardium / diagnostic imaging
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Pericardium / immunology*
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Pleura / diagnostic imaging
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Pleura / immunology*
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Pleural Effusion / diagnosis
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Pleural Effusion / drug therapy
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Pleural Effusion / immunology*
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Tomography, X-Ray Computed
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Treatment Outcome
Substances
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Biomarkers
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Immunoglobulin G
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Immunosuppressive Agents