Larsen syndrome: a review of the literature and case report

Spec Care Dentist. 2010 Nov-Dec;30(6):255-60. doi: 10.1111/j.1754-4505.2010.00163.x. Epub 2010 Oct 19.

Abstract

Larsen syndrome is a rare genetic disorder characterized by multiple dislocations of the large joints and characteristic craniofacial abnormalities. It exists in both a severe autosomal recessive form and a mild autosomal dominant variety. To date, only three authors have reported oral findings for this syndrome. This paper describes an 8-year-old Chinese boy with Larsen syndrome who had advanced periodontitis. The need for periodontal therapy and regular monitoring of such patients has been highlighted.

Publication types

  • Case Reports

MeSH terms

  • Child
  • Cleft Lip / complications
  • Cleft Palate / complications
  • Craniofacial Abnormalities / complications
  • Dental Care for Children / methods*
  • Dental Care for Disabled / methods
  • Dentition, Mixed
  • Humans
  • Joint Dislocations / complications
  • Joint Dislocations / congenital
  • Male
  • Oral Hygiene
  • Osteochondrodysplasias / complications
  • Periodontitis / complications*
  • Periodontitis / therapy
  • Tooth Abnormalities / complications

Supplementary concepts

  • Larsen syndrome, dominant type