ENT management of a child with CHARGE association

Asian J Surg. 2004 Apr;27(2):141-3. doi: 10.1016/S1015-9584(09)60329-8.

Abstract

The acronym CHARGE is used to describe specific congenital birth defects in children: colobomata, heart defect, atresia of the choanae, retarded growth or development, genital hypoplasia, and ear anomalies or deafness. CHARGE association with hearing impairment is a challenge to ENT surgeons. We report the case of a child with CHARGE association who underwent cochlear implantation using an unconventional surgical approach and review the postoperative speech perception results. The benefits of cochlear implantation in children with multiple congenital defects are discussed.

Publication types

  • Case Reports

MeSH terms

  • Child, Preschool
  • Cochlear Implantation*
  • Developmental Disabilities / complications
  • Ear Diseases / complications
  • Ear Diseases / surgery*
  • Hearing Loss, Bilateral / etiology
  • Hearing Loss, Bilateral / surgery*
  • Humans
  • Male
  • Syndrome
  • Treatment Outcome