Caroli Disease

Congenital cystic dilatation of the intrahepatic bile ducts (BILE DUCTS, INTRAHEPATIC). It consists of 2 types: simple Caroli disease is characterized by bile duct dilatation (ectasia) alone; and complex Caroli disease is characterized by bile duct dilatation with extensive hepatic fibrosis and portal hypertension (HYPERTENSION, PORTAL). Benign renal tubular ectasia is associated with both types of Caroli disease.

Year introduced: 2004 (1993)

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Do not include MeSH terms found below this term in the MeSH hierarchy.

Tree Number(s): C06.130.120.127.500, C06.198.184.500, C16.131.077.245.250, C16.131.314.184.500, C16.320.184.250

MeSH Unique ID: D016767

Entry Terms:

• Disease, Caroli
• Caroli's Syndrome
• Carolis Syndrome
• Caroli Syndrome
• Syndrome, Caroli's
• Caroli's Disease
• Carolis Disease
• Disease, Caroli's

Previous Indexing:

• Bile Duct Diseases/congenital (1966-1992)
• Bile Ducts, Intrahepatic/abnormalities (1985-1992)
• Biliary Dyskinesia (1966-1984)

All MeSH Categories
Diseases Category
Digestive System Diseases
Biliary Tract Diseases
Bile Duct Diseases
Choledochal Cyst
Caroli Disease

All MeSH Categories
Diseases Category
Digestive System Diseases
Digestive System Abnormalities
Choledochal Cyst
Caroli Disease

All MeSH Categories
Diseases Category
Congenital, Hereditary, and Neonatal Diseases and Abnormalities
Congenital Abnormalities
Abnormalities, Multiple
Ciliopathies
Caroli Disease

All MeSH Categories
Diseases Category
Congenital, Hereditary, and Neonatal Diseases and Abnormalities
Congenital Abnormalities
Digestive System Abnormalities
Choledochal Cyst
Caroli Disease

All MeSH Categories
Diseases Category
Congenital, Hereditary, and Neonatal Diseases and Abnormalities
Genetic Diseases, Inborn
Ciliopathies
Caroli Disease